Quiz Form

Question Date: 30/11/2023

Question: A 10 years old boy presents with GTCS, h/o multifoal Myoclonus since last 2 yrs duration. For past 6m gradual decline in scholastic performance. Brother has similar epilepsy and was vaccinated per schedule. What is likely diagnosis?

Options:

Subacute Sclerosing Pan-Encephalitis
Juvenile myoclonic epilepsy
Progressive Myoclonic Epilepsy
Idiopathic occipital epilepsy

Correct Answer: Progressive Myoclonic Epilepsy

View Image: Image_202311160803526555cce8a36a3.png

Explaination: EEG features in PME: Background slowing Frequent generalized and multifocal epileptiform discharges Periodic epileptiform discharges in advanced stages of PME Photosensitivity may be notes at Low frequency of PS Continuous occipital spikes associated with photosensitivity in EEG may predict the visual failure in NCL

Reference: Satishchandra P, Sinha S. Progressive myoclonic epilepsy. Neurol India 2010