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Question
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Patients who develop symptomatic Huntington disease before the age of 20 years typically have which of the following manifestations?
Explanation
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Younger patients who develop Huntington disease during the first 2 decades of life typically have the Westphal variant, which includes parkinsonism as one of its features
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Reference
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Walker RH. Chorea. Continuum (Minneap Minn). 2013 Oct19(5 Movement Disorders)1242-63. doi 10.121201.CON.0000436155.46909.c3. PMID 24092289.
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Option 1
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Is Correct (Option 1):
Myoclonus
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Option 2
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Is Correct (Option 2):
Myopathy
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Option 3
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Is Correct (Option 3):
Parkinsonism
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Option 4
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Is Correct (Option 4):
Tremor
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