Question Date: 08/09/2023
Question: Batwings dilatation of sylvian fissures is seen in?
Options:
Correct Answer: Glutaric aciduria type I
Explaination: Batwing appearance of sylvian fissure due to atrophy is seen in glutaric acidemia type 1
Reference: Ashraf V V, Sudha K. "Batwings dilatation" of sylvian fissures in glutaric aciduria type I. Ann Indian Acad Neurol 200710189-90